Sapropterin powder packet - oral
Sapropterin powder packet - oral
This medication is used along with diet changes for long-term treatment of a certain inherited disorder (phenylketonuria-PKU). It helps remove a certain chemical (phenylalanine) from the body. Too much phenylalanine in the body can cause brain damage.
Read the Patient Information Leaflet and Instructions for Use if available from your pharmacist before you start taking sapropterin and each time you get a refill. If you have any questions, ask your doctor or pharmacist.
Take this medication by mouth with a meal as directed by your doctor, usually once daily. The dosage is based on your medical condition, age, weight, lab tests, and response to treatment.
Open the packet and pour its contents into 120 to 240 milliliters (4 to 8 ounces) of water or apple juice. Stir well until the powder dissolves completely (2 to 3 minutes). Drink all of the mixture within 30 minutes of mixing. You may also mix the powder in a small amount of soft food (such as apple sauce or pudding). Eat all of the mixture right away. Do not prepare a supply in advance.
If the dose is less than a full packet, ask your doctor or pharmacist how much water or apple juice you should use to mix with the dose. Mix the entire contents of the packet in water or apple juice as directed by your doctor. Mix well and measure the dose using a special measuring device. Do not use a household spoon because you may not get the correct dose. Take the dose within 30 minutes of mixing. Discard any unused medication.
Use this medication regularly to get the most benefit from it. To help you remember, take it at the same time each day.
Tell your doctor if you do not get better or if you get worse.
Runny/stuffy nose or sore throat may occur. If any of these effects last or get worse, tell your doctor or pharmacist promptly.
Tell your doctor right away if you have any serious side effects, including:
In the US -
Before taking sapropterin, tell your doctor or pharmacist if you are allergic to it; or if you have any other allergies. This product may contain inactive ingredients, which can cause allergic reactions or other problems. Talk to your pharmacist for more details.
Before using this medication, tell your doctor or pharmacist your medical history, especially of:
During pregnancy, this medication should be used only when clearly needed. Discuss the risks and benefits with your doctor.
It is unknown if this medication passes into breast milk. Consult your doctor before breast-feeding.
If someone has overdosed and has serious symptoms such as passing out or trouble breathing, call 911. Otherwise, call a poison control center right away. US residents can call their local poison control center at 1-800-222-1222. Canada residents can call a provincial poison control center.
Do not share this medication with others.
Lab and/or medical tests (such as phenylalanine blood levels) should be done while you are taking this medication. Keep all medical and lab appointments. Consult your doctor for more details.
If you miss a dose, take it as soon as you remember. If it is near the time of the next dose, skip the missed dose. Take your next dose at the regular time. Do not double the dose to catch up.
Information last revised April 2018.
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